Revised upper limb module for spinal muscular atrophy: Development of a new module.

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Abstract

There is a growing need for a robust clinical measure to assess upper limb motor function in spinal muscular atrophy (SMA), as the available scales lack sensitivity at the extremes of the clinical spectrum. We report the development of the Revised Upper Limb Module (RULM), an assessment specifically designed for upper limb function in SMA patients.

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Journal

Journal ID (iso-abbrev): Muscle Nerve

Title: Muscle & nerve

Publisher: Wiley-Blackwell

ISSN (Electronic): 1097-4598

ISSN (Print): 0148-639X

Publication date (Electronic): Jun 2017

Volume: 55

Issue: 6

Affiliations

[1 ] Department of Paediatric Neurology, Catholic University, Largo Gemelli 8, 00168, Rome, Italy.

[2 ] Institute of Genetic Medicine, Newcastle University, Newcastle, United Kingdom.

[3 ] Department of Neurology, Columbia University Medical Center, New York, USA.

[4 ] Dubowitz Neuromuscular Centre, UCL Institute of Child Health & Great Ormond Street Hospital, London, United Kingdom.

[5 ] Department of Neurology, Boston Children's Hospital, Harvard Medical School, Boston, Massachusetts, USA.

[6 ] Division of Neurology, Children's Hospital of Philadelphia and Departments of Neurology and Pediatrics, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, USA.

[7 ] Division of Neurology, Nemours Children's Hospital, Orlando, Florida, USA.

[8 ] Department of Neurology, Stanford University, Stanford, California, USA.

[9 ] Department of Clinical and Experimental Medicine and Nemo Sud Clinical Centre, University of Messina, Italy.

Article

DOI: 10.1002/mus.25430

PubMed ID: 27701745

SO-VID: f784a0c6-9cea-4f7b-bff4-5eb229f55fbe

History

Keywords: Hammersmith functional motor scale,Rasch analysis,functional assessment,outcome measures,spinal muscular atrophy,upper limb function

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Keywords: Hammersmith functional motor scale, Rasch analysis, functional assessment, outcome measures, spinal muscular atrophy, upper limb function

Revised upper limb module for spinal muscular atrophy: Development of a new module.

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